{"id":6278,"date":"2024-10-19T11:55:48","date_gmt":"2024-10-19T11:55:48","guid":{"rendered":"https:\/\/autism.fratnow.com\/blog\/?p=6278"},"modified":"2024-10-19T11:55:48","modified_gmt":"2024-10-19T11:55:48","slug":"pans-pandas-diagnosis-and-possible-treatments","status":"publish","type":"post","link":"https:\/\/autism.fratnow.com\/blog\/pans-pandas-diagnosis-and-possible-treatments\/","title":{"rendered":"PANS\/PANDAS \u2013 Diagnosis and Possible Treatments"},"content":{"rendered":"<p>[vc_row][vc_column][vc_single_image image=&#8221;6279&#8243; img_size=&#8221;full&#8221;][\/vc_column][\/vc_row][vc_row][vc_column][vc_custom_heading text=&#8221;Introduction&#8221;][vc_column_text single_style=&#8221;&#8221;]<\/p>\n<p class=\"p-mr-bottom-10\">A few months ago, we discussed a unique condition that is referred to as PANS\/PANDAS. As a reminder:<\/p>\n<p>[\/vc_column_text][vc_column_text single_style=&#8221;&#8221;]<\/p>\n<p class=\"p-mr-bottom-10\">PANS (Pediatric Acute-onset Neuropsychiatric Syndrome) and PANDAS (Pediatric Autoimmune Neuropsychiatric Disorders Associated with Streptococcal Infections) are a set of pediatric neuropsychiatric disorders. These disorders are characterized by the sudden onset of obsessive-compulsive disorder (OCD) or eating disorders, along with other neuropsychiatric symptoms, such as tics, anxiety, irritability, and emotional lability. Typically, these symptoms emerge at a very young age, usually between 3 to puberty.<\/p>\n<p>[\/vc_column_text][vc_column_text single_style=&#8221;&#8221;]<\/p>\n<p class=\"p-mr-bottom-10\">The key difference between PANS and PANDAS lies in their trigger factors:<\/p>\n<p>[\/vc_column_text][vc_column_text single_style=&#8221;&#8221;]<\/p>\n<ul class=\"mr-left-ul-40\">\n<li><strong>PANS:<\/strong> This term encompasses cases where the sudden onset of symptoms occurs without a known infectious trigger. While infections can still play a role, they might not always be directly linked to the symptoms.<\/li>\n<li><strong>PANDAS: <\/strong>In these cases, the onset of symptoms is associated with a streptococcal infection, particularly group A streptococcal infections, such as strep throat. The theory behind PANDAS is that the body\u2019s immune response to the streptococcal infection leads to an autoimmune reaction, where antibodies mistakenly attack certain brain structures, resulting in neuropsychiatric symptoms.<\/li>\n<\/ul>\n<p>[\/vc_column_text][vc_column_text single_style=&#8221;&#8221;]<\/p>\n<p class=\"p-mr-bottom-10\">Interestingly, a recent publication examined the role of folate receptor autoantibodies in this population. The paper reviewed the role of FRAT<sup>\u00ae<\/sup> (Folate Receptor Autoantibody Test) as a supplementary tool in providing a possible marker and aiding in the <a href=\"https:\/\/autism.fratnow.com\/blog\/pans-pandas-symptoms-diagnosis-treatment-research\/\" target=\"_blank\" rel=\"noopener\">treatment of PANS\/PANDAS<\/a> with folinic acid. The study revealed a FRAA (Folate receptor autoantibodies) prevalence of 63.8% within the sample population. More importantly, it highlighted a case study of an 18-year-old male with PANS who suffered from severe OCD and anxiety. His symptoms improved significantly after leucovorin was introduced to address a positive binding FRAA. This case was particularly noteworthy, as the patient was initially unable to tolerate antimicrobial treatment\u2014an essential component in PANS management. However, after addressing his central folate metabolism abnormalities, he became more tolerant of antimicrobials, allowing for treatment of the underlying infections contributing to PANS. This is the first documented report linking FRAAs to PANS\/PANDAS. These findings suggest that children and adolescents with PANS\/PANDAS should be screened using FRAT<sup>\u00ae<\/sup>, and if positive FRAAs are identified, appropriate treatment should be considered to manage symptoms (mainly the use of folinic acid).<\/p>\n<p>[\/vc_column_text][\/vc_column][\/vc_row][vc_row][vc_column][vc_column_text single_style=&#8221;&#8221;]<\/p>\n<p class=\"p-mr-bottom-10\">Essentially, folinic acid can be beneficial for children with PANS (Pediatric Acute-Onset Neuropsychiatric Syndrome) and PANDAS (Pediatric Autoimmune Neuropsychiatric Disorders Associated with Streptococcal Infections) by addressing potential folate transport issues in the brain. Here&#8217;s how folinic acid may help:<\/p>\n<p>[\/vc_column_text][\/vc_column][\/vc_row][vc_row][vc_column][vc_custom_heading text=&#8221;1. Bypassing Folate Receptor Blockade&#8221;][vc_column_text single_style=&#8221;&#8221;]<\/p>\n<ul class=\"mr-left-ul-40\">\n<li>In some children with PANS\/PANDAS, autoantibodies against the folate receptor alpha (FR\u03b1) can block the transport of folate into the brain. This leads to reduced folate levels in the central nervous system, which is important for brain function and development.<\/li>\n<li>Folinic acid (a form of folate) can bypass the blocked folate receptors more effectively than regular folic acid, helping to increase folate levels in the brain despite the presence of the autoantibodies.<\/li>\n<\/ul>\n<p>[\/vc_column_text][\/vc_column][\/vc_row][vc_row][vc_column][vc_custom_heading text=&#8221;2. Improving Neurological Function&#8221;][vc_column_text single_style=&#8221;&#8221;]<\/p>\n<ul class=\"mr-left-ul-40\">\n<li>Folate is crucial for neurotransmitter production, myelin synthesis, and DNA repair. Restoring folate levels with folinic acid can support these processes, improving cognitive function, mood regulation, and reducing neuropsychiatric symptoms such as anxiety, obsessive-compulsive behaviors, or tics.<\/li>\n<\/ul>\n<p>[\/vc_column_text][\/vc_column][\/vc_row][vc_row][vc_column][vc_custom_heading text=&#8221;3. Modulating Immune Function&#8221;][vc_column_text single_style=&#8221;&#8221;]<\/p>\n<ul class=\"mr-left-ul-40\">\n<li>Folinic acid has been shown to modulate immune responses, potentially reducing the autoimmune inflammation that is thought to contribute to the neuropsychiatric symptoms in PANS\/PANDAS. By supporting immune regulation, folinic acid may reduce the severity of autoimmune attacks on the brain.<\/li>\n<\/ul>\n<p>[\/vc_column_text][\/vc_column][\/vc_row][vc_row][vc_column][vc_custom_heading text=&#8221;4. Supporting Mitochondrial Function&#8221;][vc_column_text single_style=&#8221;&#8221;]<\/p>\n<ul class=\"mr-left-ul-40\">\n<li>Folate is also important for mitochondrial energy production. Folinic acid can help improve mitochondrial function in brain cells, which may be impaired in children with PANS\/PANDAS, potentially leading to better mental clarity, focus, and energy.<\/li>\n<\/ul>\n<p>[\/vc_column_text][\/vc_column][\/vc_row][vc_row][vc_column][vc_custom_heading text=&#8221;5. Reducing Symptoms of Cerebral Folate Deficiency&#8221;][vc_column_text single_style=&#8221;&#8221;]<\/p>\n<ul class=\"mr-left-ul-40\">\n<li>Children with PANS\/PANDAS who have <a href=\"https:\/\/autism.fratnow.com\/blog\/cerebral-folate-deficiency-an-overview\/\" target=\"_blank\" rel=\"noopener\">cerebral folate deficiency<\/a> (due to FR\u03b1 autoantibodies) may exhibit symptoms such as developmental regression, speech issues, irritability, and mood swings. Folinic acid can alleviate these symptoms by ensuring adequate folate levels in the brain.<\/li>\n<\/ul>\n<p>[\/vc_column_text][\/vc_column][\/vc_row][vc_row][vc_column][vc_column_text single_style=&#8221;&#8221;]<\/p>\n<p class=\"p-mr-bottom-10\">Of course, further research is needed in the PANS\/PANDAS population, but this is a great start! Systematic clinical studies demonstrating leucovorin\u2019s effectiveness in FRAA-positive PANS\/PANDAS patients would be valuable in supporting treatment recommendations involving leucovorin in this population. Let\u2019s hope this research continues. It is very promising!<\/p>\n<p>[\/vc_column_text][\/vc_column][\/vc_row][vc_row][vc_column][vc_custom_heading text=&#8221;References&#8221;][vc_column_text single_style=&#8221;&#8221;]<\/p>\n<div id=\"blog-ref-3564\">\n<ol class=\"ul-36784\">\n<li><a href=\"https:\/\/www.mdpi.com\/2075-4426\/14\/2\/166\" target=\"_blank\" rel=\"nofollow noopener\">https:\/\/www.mdpi.com\/2075-4426\/14\/2\/166<\/a><\/li>\n<\/ol>\n<\/div>\n<p>[\/vc_column_text][\/vc_column][\/vc_row]<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Folinic acid aids PANS\/PANDAS treatment by bypassing folate receptor autoantibodies, improving brain function, and reducing neuropsychiatric symptoms.<\/p>\n","protected":false},"author":4,"featured_media":6279,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[70],"tags":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v21.3 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>PANS\/PANDAS \u2013 Diagnosis and Possible Treatments - 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